Patient | Age of diagnosis | Follow-up (years) | Ethnicity | Symptom duration before diagnosis (weeks) | Clinical features and serology at SLE diagnosis | CYC post-BCDT | AZA post-BCDT | MMF post-BCDT | Additional RTX |
---|---|---|---|---|---|---|---|---|---|
1 | 36 | 5 | Caucasian | 5 | Arthritis, fatigue, ANA, ↑ anti-dsDNA, lymphopenia, ↓ C3 | Yes | Yes | No | No |
2 | 31 | 7 | Caucasian | 384 | Discoid lupus, malar rash, Raynaud's, alopecia, pleurisy, ↑ anti-dsDNA, lymphopenia | Yes | Yes | No | No |
3 | 26 | 6 | Malaysian/Chinese | 16 | Discoid lupus, alopecia, Raynaud's, arthralgia, ANA, anti-SM, lymphopenia | No | Yes | No | No |
4 | 39 | 6 | Caucasian | 40 | Arthritis, serosits, ANA, ↑ anti-dsDNA, lymphopenia, ↑aCL | Yes | Yes | No | No |
5 | 47 | 7 | African-Caribbean | 12 | Arthritis, rash, alopecia, ANA, lymphopenia | No | No | No | No |
6 | 21 | 1 | Chinese | 4 | Rash, fever, angiooedema, arthritis, ANA, ↑ anti-dsDNA, lymphopenia, ↓ C3 | Yes | Yes | No | No |
7 | 34 | 3 | African-Caribbean | 6 | Arthritis, rash, alopecia, ANA, lymphopenia | Yes | No | No | Yes |
8 | 47 | 6 | African-Caribbean | 6 | Fever, fatigue, alopecia, rash, arthritis, serositis, ANA, anti-CCP | Yes | Yes | No | No |
9 | 44 | 5 | Caucasian | 4 | Livedo reticularis, serositis, rash, proteinuria, ANA, ↑ anti-dsDNA, lymphopenia, ↓ C3, ↑aCL and LA | Yes | Yes | No | No |
10 | 29 | 5 | African-Caribbean | 6 | Arthritis, rash, alopecia, ↑ anti-dsDNA, ↓ C3, ANA, RNP | Yes | Yes | yes | Yes |
11 | 50 | 5 | Caucasian | 12 | Raynaud's, ANA, Ro, arthritis, mouth ulcers, photosensitivity, rash, Sjögren's syndrome | Yes | Yes | No | Yes |
12 | 26 | 1 | Caucasian | 20 | Arthritis, ANA, p-ANCA, ↑ anti-dsDNA, anti-SM, RNP, ↓ C3 | No | Yes | No | No |
13 | 34 | 2 | Caucasian | 2 | Arthritis, ANA, rash, Sjögren's syndrome, ↑ anti-dsDNA, ↓ C3, renal failure | Yes | No | yes | No |
14 | 25 | 6 | Caucasian | 8 | Arthritis, rash, fever, ANA, ↑ anti-dsDNA, anti-SM, RNP, ↓ C3 | Yes | No | yes | Yes |
15 | 28 | 2 | Asian | 4 | Arthritis, fatigue, fever, lymphadenopathy, ANA, pleurisy, Ro, LA, SM and RNP, ↓ C3 | Yes | Yes | No | No |
16 | 32 | 6 | Caucasian | 2 | Arthritis, headache, Ro, LA, ANA, ↑ anti-dsDNA | Yes | No | No | No |
aCL, antiocardiolipin antibody; ANCA, antineutrophil cytoplasmic antibody; AZA, azathioprine; BCD, B-cell depletion; BCDT, B-cell depletion treatment; CCP, cyclic citrullinated protein; CYC, cyclophosphamide; dsDNA, double-stranded DNA; LA, anti-La antibody; MMF, mycophenolate mofetil; RNP, anti-ribonucleic antibody; RTX, rituximab; SM, anti-Smith antibody.