Criteria | Criteria items | Alopecia as a criterion |
1971 ACR | 6 cutaneous items (malar rash, discoid rash*, Raynaud’s phenomenon, alopecia, photosensitivity, oral/nasopharyngeal ulcers). | Rapid loss of a large amount of scalp hair, by patient’s history or physician’s observation.† |
1982 ACR | 4 cutaneous items (malar rash, discoid rash*, photosensitivity, oral ulcers). | Criteria do not include alopecia as an item. |
1997 ACR | 4 cutaneous items (malar rash, discoid rash*, photosensitivity, oral ulcers). | Criteria do not include alopecia as an item. |
2012 SLICC | 4 cutaneous items (acute cutaneous lupus erythematosus, subacute cutaneous lupus erythematosus*, oral ulcers, non-scarring alopecia). | Diffuse thinning or hair fragility with visible broken hairs in the absence of other causes such as alopecia areata, drugs, iron deficiency and androgenetic alopecia.† |
*Can also present clinically as alopecia.
†Definition does not require histopathological/immunopathological confirmation.
ACR, American College of Rheumatology; SLICC, Systemic Lupus International Collaborating Clinics.