Table 3

Extrarenal manifestations

PatientN, SexAge at TAC starting (years)Disease duration(years)Main indication for TACExtrarenal featuresConcomitant therapiesOutcome (PGA)
1, M188NephritisArthritis, lymphopaeniaGC, HCQ, MMFRenal: non-responder; Extrarenal: non-responder
2, F5313ExtrarenalCytopenia (Evans Syndrome)GC, HCQNon-responder
3, F2914ExtrarenalSerositis, lymphopaenia, arthritisGC, HCQComplete response at 6 months
4, F215ExtrarenalArthritis, skin rash CytopeniaGC, HCQComplete response at 3 months
5, F3510ExtrarenalSkin vasculitisGC, HCQ, MMF, BelimumabNon-responder
6, F633NephritisAnaemia, serositisGC, HCQ, MMFComplete response at 3 months
7, F3213ExtrarenalArthritisGC, HCQ, MMFPartial response at 3 months
8, F3517Nephritis neutropaeniaNeutropaeniaGC, AZAPartial response at 3 months
  • AZA, azathioprine; GC, glucocorticoids; HCQ, hydroxychloroquine; MMF, mycophenolate mofetil; TAC, Tacrolimus; PGA, physician global assessment.